Współtwórca:

Mossakowski Medical Research Center Polish Academy of Sciences. Department of Neuromuscular

Miejsce wydania:

Warsaw

Opis:

Muscle segment examination in light & electon microscopy

Abstrakt:

A 7-year-old patinet with limb-gridle muscular dystrophy was examined. A biopsy of quadriceps sinister was performed. Electronmicroscopy analysis of the biopsy revealed some fibers of the correct diameter, preserved myofbrils structure and typical, located under the sarcolemma nuclei. In some fibers fat droplets were seen. Significantly damaged, swollen mitochondria characterized by loss of mitochondrial cristae were observed. Except fibers of the correct diameter and preserved myofibrils, small fibers with disurbed sarcomere strucure and centrally located abnormal nuclei were visible. Some of the fibers showed abnormalities and discrupture of the contractile apparatus. The image of changes suggests primary muscular dmage.

Szczegółowy typ zasobu:

Photography ; Files

Format:

pdf

Identyfikator zasobu:

oai:rcin.org.pl:142187

Język:

pol

Prawa:

Creative Commons Attribution BY 4.0 license

Zasady wykorzystania:

Copyright-protected material. [CC BY 4.0] May be used within the scope specified in Creative Commons Attribution BY 4.0 license, full text available at: ; -

Digitalizacja:

Mossakowski Medical Research Institute PAS

Lokalizacja oryginału:

Library of the Mossakowski Medical Research Institute PAS

Dofinansowane ze środków:

Operational Program Digital Poland, 2014-2020, Measure 2.3: Digital accessibility and usefulness of public sector information; funds from the European Regional Development Fund and national co-financing from the state budget.

Dostęp:

Open